There is no link between
lymphangiomyomatosis and CF. Lymphangiomyomatosis may cause chylothorax.
Hemoptysis (either scanty or profuse) and spontaneous pneumothorax are
well-known complications of CF. Atelectasis can result from the mucus plugging
of airways. Acute or chronic respiratory failures are also seen commonly in CF
patients, as are pulmonary infections due to pseudomonads or staphylococci. CF
patients are prone to develop allergic bronchopulmonary aspergillosis, which
requires treatment with corticosteroids. Hypertrophic pulmonary osteoarthopathy,
which is a triad of digital clubbing, arthritis, and periostitis, can occur in CF
and is clearly associated with severity of pulmonary disease. In hypertrophic
pulmonary osteoarthopathy, the long and tubular bones are most often affected.
Hypertrophic pulmonary osteoarthopathy is treated with anti-inflammatory agents
for symptomatic relief.
- Lymphangiomyomatosis and chylothorax.
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