Turner White CommunicationsAbout TWCSubscribeContact TWCHomeSearch
Hospital PhysicianJCOMSMPBRMsCart
Current Contents
Past Issue Archives
Interactive:
Self-Assessment Questions
Review of
Clinical Signs
Clinical Review
Quiz
Pediatric Rounds
Resident Grand Rounds
Article Archives
Case Reports
Clinical Practice
Exams
Pediatric Rounds
Resident Grand Rounds
Review of
Clinical Signs

Guide to Reading
Hospital Physician
Editorial Board
Information for Authors

Reprints, Permissions, & Copyright
Site Map
Self-Assessment Questions

Obstetrics & Gynecology


Answer 5
  1. Rokitansky-Küster-Hauser syndrome (vaginal and uterine agenesis). The fact that this patient has normally developed secondary sex characteristics proves that the hypothalamic-pituitary-ovarian function is normal. Patients with testicular feminization syndrome do not have pubic or axillary hair. In this syndrome, testicles produce testosterone but the target cells in the hair follicles are believed to lack androgen receptors. Patients with an imperforate hymen usually complain of cyclic lower abdominal pain that worsens progressively because of uterine and vaginal distention with accumulated obstructed menstrual flow. The remaining diagnosis is genital tract anomaly, the most common of which is vaginal agenesis. Patients with congenital absence of the vagina usually lack a uterus as well and are likely to seek medical advice for primary amenorrhea at puberty or later, as this patient did. The development of secondary sex characteristics, ovaries, and sex chromosome complement is normal in patients with Rokitansky-Küster-Hauser syndrome.

Click here to return to the questions

 

Hospital Physician     JCOM     Seminars in Medical Practice
Hospital Physician Board Review Manuals
About TWC    Subscribe    Contact TWC    Home    Search   Site Map

Copyright © 2009, Turner White Communications
Updated 1/04/08 • kkj