An 18-Month-Old Child with a Previously Undiagnosed Fatty Acid Oxidation Disorder Mark A. Hostetler, MD, MPH Dr. Hostetler is an Assistant Professor; Chief of the Section of Emergency Medicine, Department of Pediatrics; and Medical Director of the Pediatric Emergency Department, University of Chicago Children’s Hospital, Chicago, IL. The questions below are based on the June 2003 Pediatric Rounds article, “An 18-Month-Old Child with a Previously Undiagnosed Fatty Acid Oxidation Disorder.” Choose the single best answer for each question.
	1. Which of the following is the appropriate treatment for symptomatic hypoglycemia in a 12-month-old child? 2 mL/kg of 50% dextrose solution 2 mL/kg of 25% dextrose solution 2 mL/kg of 5% dextrose solution 20 mL/kg of normal saline solution Click here to compare your answer. 2. Which of the following is a cause of hypoglycemia in children? Acetaminophen ingestion Alcohol ingestion Closed head injury New-onset diabetes Click here to compare your answer.		3. Which of the following best describes the constellation of metabolic disturbances associated with fatty acid oxidation disorders? Ketoacidosis with a high anion gap Hypoketotic hypoglycemia with normal to moderately elevated ammonia level Hypoketotic hypoglycemia with markedly elevated ammonia level Normoglycemia with markedly elevated ammonia level Click here to compare your answer. 4. Which of the following is the most common of the fatty acid oxidation disorders? Medium-chain acyl-CoA dehydrogenase (MCAD) deficiency Very long-chain acyl-CoA dehydrogenase (VLCAD) deficiency Carnitine palmitoyltransferase (CPT) I deficiency Carnitine palmitoyltransferase (CPT) II deficiency Click here to compare your answer.
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